• CLN6 Polyclonal Antibody
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Upingbio

YP-Ab-03777-100UL

CLN6 Polyclonal Antibody

CLN6 Polyclonal Antibody

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  • Gene Name: CLN6
  • Immunogen: The antiserum was produced against synthesized peptide derived from human CLN6. AA range:221-270
  • Specificity: CLN6 Polyclonal Antibody detects endogenous levels of CLN6 protein.
  • Composition: Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • Source: Polyclonal, Rabbit,IgG
  • Dilution ratio: WB: 1/500 - 1/2000. IHC: 1/100 - 1/300. ELISA: 1/40000.. IF 1:50-200
  • Purification process: The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
  • Concentration: 1 mg/ml
  • Storage: -20°C/1 year
  • Other Names: CLN6; Ceroid-lipofuscinosis neuronal protein 6; Protein CLN6
  • Background: This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function. [provided by RefSeq, Oct 2008],
  • Function: disease:Defects in CLN6 are the cause of variant late-onset infantile neuronal ceroid lipofuscinosis (vLINCL) [MIM:601780].,online information:Neural Ceroid Lipofuscinoses mutation db,
  • Species: Human;Rat;Mouse;
  • Range: WB;IHC;IF;ELISA
  • Protein: Ceroid-lipofuscinosis neuronal protein 6
  • DA: 40kD
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