anti- HPS1 antibody

anti- HPS1 antibody

Product Name

HPS1 antibody

Size

100µg

Form

liquid

Purification

Immunogen affinity purified

Purity

≥95% as determined by SDS-PAGE

Host

Rabbit

Clonality

polyclonal

Isotype

IgG

Storage

PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20℃ for 12 months (Avoid repeated freeze / thaw cycles.)

BACKGROUND

This gene encodes a protein that may play a role in organelle biogenesis associated with melanosomes, platelet dense granules, and lysosomes. The encoded protein is a component of three different protein complexes termed biogenesis of lysosome-related organelles complex (BLOC)-3, BLOC4, and BLOC5. Mutations in this gene are associated with Hermansky-Pudlak syndrome type 1. Alternative splicing results in multiple transcript variants. A pseudogene related to this gene is located on chromosome 22.

IMMUNOGEN INFORMATION

Immunogen

Hermansky-Pudlak syndrome 1

Synonyms

HPS

Observed MW

70-79 kDa

APPLICATION

Tested Application

ELISA, WB, IHC, IF

Recommended Dilution

WB: 1:500 - 1:2000; IHC: 1:50 - 1:100; IF: 1:50 - 1:100

UNIPROT INFORMATION

UniProt ID

Q92902

IMAGES

Immunohistochemistry of paraffin-embedded rat kidney using FNab03998(HPS1 antibody) at dilution of 1:100

L02 cells were subjected to SDS PAGE followed by western blot with FNab03998(HPS1 antibody) at dilution of 1:800