anti- MCCC2 antibody

anti- MCCC2 antibody

Product Name

MCCC2 antibody

Size

100µg

Form

liquid

Purification

Immunogen affinity purified

Purity

≥95% as determined by SDS-PAGE

Host

Rabbit

Clonality

polyclonal

Isotype

IgG

Storage

PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20℃ for 12 months (Avoid repeated freeze / thaw cycles.)

BACKGROUND

This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.

IMMUNOGEN INFORMATION

Immunogen

methylcrotonoyl-Coenzyme A carboxylase 2 (beta)

Synonyms

MCCB

Observed MW

61 kDa

APPLICATION

Tested Application

ELISA, WB, IHC

Recommended Dilution

WB: 1:500 - 1:2000; IHC: 1:50 - 1:200

UNIPROT INFORMATION

UniProt ID

Q9HCC0

IMAGES

Immunohistochemistry of paraffin-embedded rat brain using FNab05048(MCCC2 antibody) at dilution of 1:100

human liver tissue were subjected to SDS PAGE followed by western blot with FNab05048(MCCC2 antibody) at dilution of 1:1000