anti- SGSH antibody

anti- SGSH antibody

Product Name

SGSH antibody

Size

100µg

Form

liquid

Purification

Immunogen affinity purified

Purity

≥95% as determined by SDS-PAGE

Host

Rabbit

Clonality

polyclonal

Isotype

IgG

Storage

PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20℃ for 12 months (Avoid repeated freeze / thaw cycles.)

BACKGROUND

This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.

IMMUNOGEN INFORMATION

Immunogen

N-sulfoglucosamine sulfohydrolase

Synonyms

HSS

Observed MW

57 kDa

APPLICATION

Tested Application

ELISA, WB, IHC

Recommended Dilution

WB: 1:500 - 1:2000; IHC: 1:50 - 1:100

UNIPROT INFORMATION

UniProt ID

P51688

IMAGES

Immunohistochemistry of paraffin-embedded human stomach using FNab07813( SGSH Antibody) at dilution of 1:50

HEK-293 cells were subjected to SDS PAGE followed by western blot with FNab07813( SGSH Antibody) at dilution of 1:1000