GAA Antibody

Size

100ug

Clone Number

Aliases

70 kDa lysosomal alpha-glucosidase antibody; Acid alpha glucosidase antibody; Acid maltase antibody; Aglucosidase alfa antibody; Alpha glucosidase antibody; GAA antibody; Glucosidase alpha acid (Pompe disease glycogen storage disease type II) antibody; Glucosidase alpha acid antibody; Glucosidase alpha antibody; LYAG antibody; LYAG_HUMAN antibody; Lysosomal alpha glucosidase antibody

Immunogen Species

Homo sapiens (Human)

UniProt ID

P10253

Immunogen

Recombinant Human Lysosomal alpha-glucosidase protein (601-952AA)

Raised in

Rabbit

Species Reactivity

Human, Mouse

Tested Applications

ELISA, WB, IHC, IF; Recommended dilution: WB:1:1000-1:5000, IHC:1:20-1:200, IF:1:50-1:200

Background

Essential for the degradation of glygogen to glucose in lysosomes.

Clonality

Polyclonal

Isotype

IgG

Purification Method

>95%, Protein G purified

Conjugate

Non-conjugated

Buffer

Preservative: 0.03% Proclin 300
Constituents: 50% Glycerol, 0.01M PBS, PH 7.4

Form

Liquid

Stroage

Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.

Target Names

GAA

Research Areas

Metabolism; Signal transduction