CLN6 Polyclonal Antibody

Ab type

Primary antibody

Background

CLN6 (ceroid-lipofuscinosis, neuronal 6, late infantile, variant) is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function.

Reactivity

Human

Clonality

Polyclonal

Host

Rabbit

Isotype

IgG

Immunogen

The antiserum was produced against synthesized peptide derived from human CLN6. AA range:221-270

Storage Stability

-20°C for one year

Concentration

1 mg/ml

MolecularWeight_Da

35919

synonyms

CLN6; Ceroid-lipofuscinosis neuronal protein 6; Protein CLN6