ABCbiolab
SKU:ABCCS58830
BCKDHA Antibody
BCKDHA Antibody
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Size
100ug
Clone Number
Aliases
Branched chain alpha keto acid dehydrogenase E1 component alpha polypeptide antibody; FLJ45695 antibody; OVD1A antibody; 2 oxoisovalerate dehydrogenase (lipoamide) antibody; 2 oxoisovalerate dehydrogenase subunit alpha, mitochondrial antibody; 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial antibody; BCKDE1A antibody; BCKDH E1 alpha antibody; BCKDH E1-alpha antibody; BCKDHA antibody; Branched chain alpha keto acid dehydrogenase E1 component alpha chain antibody; Branched chain keto acid dehydrogenase E1 alpha polypeptide antibody; Branched chain keto acid dehydrogenase E1, alpha polypeptide (maple syrup urine disease) antibody; Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain antibody; MSU antibody; MSUD1 antibody; ODBA_HUMAN antibody
Immunogen Species
Homo sapiens (Human)
UniProt ID
P12694
Immunogen
Recombinant Human 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial protein (268-407AA)
Raised in
Rabbit
Species Reactivity
Human
Tested Applications
ELISA, WB, IHC; Recommended dilution: WB:1:500-1:5000, IHC:1:200-1:500
Background
The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3).
Clonality
Polyclonal
Isotype
IgG
Purification Method
>95%, Protein G purified
Conjugate
Non-conjugated
Buffer
Preservative: 0.03% Proclin 300
Constituents: 50% Glycerol, 0.01M PBS, pH 7.4
Form
Liquid
Stroage
Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
Target Names
BCKDHA
Research Areas
Others
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