{"product_id":"r32608","title":"GAA Antibody \/ Glucosidase alpha acid","description":"\u003cp\u003eLysosomal alpha-glucosidase is an enzyme that in humans is encoded by the GAA gene. This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants.\u003c\/p\u003e","brand":"NSJ Bioreagents","offers":[{"title":"100 ug \/ Rabbit","offer_id":49476649124120,"sku":"R32608","price":439.0,"currency_code":"USD","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0590\/5652\/1400\/files\/get_image_1e79fbab-acf1-42f0-907a-3a6d0da5c879.jpg?v=1734478645","url":"https:\/\/danabiosci.com\/products\/r32608","provider":"Dana Bioscience","version":"1.0","type":"link"}