{"product_id":"nsj-rq8619-100ug","title":"MCCC2 Antibody \/ Methylcrotonoyl-CoA carboxylase beta chain, 100 ug","description":"\u003cp\u003eThis gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. Alternative splicing results in multiple transcript variants encoding distinct isoforms.\u003c\/p\u003e","brand":"NSJ Bioreagents","offers":[{"title":"100 ug","offer_id":51549650911512,"sku":"RQ8619","price":449.0,"currency_code":"USD","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0590\/5652\/1400\/files\/get_image_2848b274-20bb-4061-bf43-05dbb3f419e6.jpg?v=1768301572","url":"https:\/\/danabiosci.com\/products\/nsj-rq8619-100ug","provider":"Dana Bioscience","version":"1.0","type":"link"}