{"product_id":"new-product-701381","title":"BCKDHB Rabbit pAb","description":"\u003cp\u003eThis gene encodes the E1 beta subunit of branched-chain keto acid dehydrogenase, which is a multienzyme complex associated with the inner membrane of mitochondria. This enzyme complex functions in the catabolism of branched-chain amino acids. Mutations in this gene have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation and feeding problems. Alternative splicing at this locus results in multiple transcript variants.\u003c\/p\u003e","brand":"Abclonal","offers":[{"title":"100ul","offer_id":48577084064024,"sku":"A10533","price":298.0,"currency_code":"USD","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0590\/5652\/1400\/files\/A10533_1.jpg?v=1717031746","url":"https:\/\/danabiosci.com\/products\/new-product-701381","provider":"Dana Bioscience","version":"1.0","type":"link"}